NOUN
- rare (usually fatal) brain disease (usually in middle age) caused by an unidentified slow virus; characterized by progressive dementia and gradual loss of muscle control
How To Use Creutzfeldt-Jakob disease In A Sentence
- Fewer and fewer cows are infected today, but now there is an outbreak of human Creutzfeldt-Jakob disease, resulting from the consumption of beef products contaminated by infected bovine central nervous system tissue.
- Design - Screening study of patients suspected clinically to have Creutzfeldt-Jakob disease and other neurodegenerative diseases by prion protein gene analysis.
- The spontaneous form of Creutzfeldt-Jakob disease, the one not linked to consumption of beef or anything else, claimed over 1,000 Brits in the same time period.
- But the news last week of a death at UW Hospital due to Creutzfeldt-Jakob disease brought to mind once again the dangers of the neurological illnesses known as transmissible spongiform encephalopathies, or TSEs. Madison.com - top
- In humans, eating meat products contaminated with the illness is linked to variant Creutzfeldt-Jakob disease, a rare and fatal malady.
- Prions cause Creutzfeldt-Jakob disease (or "mad cow disease" in cattle) by rearranging the structure of normal proteins in their own image.
- These are not the clinical features of variant Creutzfeldt-Jakob disease and, crucially, the neuropathological appearances were ‘not characteristic of Creutzfeldt-Jakob disease.’
- Transmissible spongiform encephalopathies such as mad cow disease and its human counterpart, variant Creutzfeldt-Jakob disease, are not caused by bacteria or viruses.
- For many years after their discovery as the agents of some rare neurodegenerative diseases in mammals, such as scrapie in sheep and human Creutzfeldt-Jakob disease and kuru, prions have remained a truly esoteric research topic.
- In fact, scientists now think that misshapen proteins could be the key to a host of illnesses, from Creutzfeldt-Jakob disease to cataracts and diabetes.